Background: Since testing for antineutrophil cytoplasmic antibodies (ANCA) became
available for routine evaluation, no large homogeneous cohort of patients with the Churg–Strauss …

Objective To assess the efficacy of systemic corticosteroids (CS) alone as first‐line treatment
in patients with Churg‐Strauss syndrome (CSS) without poor‐prognosis factors, as defined …

Objective Findings from the WEGENT trial and other short‐term studies have suggested that
azathioprine (AZA) or methotrexate (MTX) could effectively maintain remission of …

The respiratory manifestations of eosinophilic granulomatosis with polyangiitis (EGPA) have
not been studied in detail. In this retrospective multicentre study, EGPA was defined by …

In this retrospective study, we analyzed 17 patients presenting with pulmonary fibrosis and
a positive ANCA testing. This group was compared with a control group of 12 patients with …

Idiopathic pulmonary fibrosis (IPF) is the most frequent chronic idiopathic interstitial pneumonia
in adults. The management of rare diseases in France has been organised by a national …

Study objectives Respiratory failure (RF) is a frequent cause of death among patients with
bilateral bronchiectasis. An ICU admission is commonly required, and neither short-term or …

Methods Seventeen patients with fire-eater’s lung were included in this study from October
1996 to January 2001. Patients were evaluated at the time of the initial accident, then at 3 and …

Aim: To describe the main characteristics and the treatment of cryptococcosis in patients with
sarcoidosis. Design: Multicenter study including all patients notified at the French National …

Antisynthetase syndrome (ASS) is characterised by an inflammatory myositis associated
with interstitial lung disease (ILD) and antisynthetase antibodies. Other symptoms, including …