Motile cilia are highly complex hair-like organelles of epithelial cells lining the surface of
various organ systems. Genetic mutations (usually with autosomal recessive inheritance) that …

… Nielsen KG, Bisgaard H. Discriminative capacity of bronchodilator response measured with
three different lung function techniques in asthmatic and healthy children aged 2 to 5 years. …

… < 30 kg) or 400 mg dosing twice daily (for patient weight >30 kg) [21]. Although CF patients
showed improvement in lung function, in PCD patients, there was no improvement in the …

Primary ciliary dyskinesia (PCD) is associated with abnormal ciliary structure and function,
which results in retention of mucus and bacteria in the respiratory tract, leading to chronic oto-…

The diagnosis of primary ciliary dyskinesia is often confirmed with standard, albeit complex
and expensive, tests. In many cases, however, the diagnosis remains difficult despite the …

… In summary, intraoperative administration of 40 mL/kg compared with 15 mL/kg LR for
laparoscopic cholecystectomy improves recovery of perioperative organ functions and reduces …

Primary ciliary dyskinesia (PCD) is a hereditary disorder of mucociliary clearance causing
chronic upper and lower airways disease. We determined the number of patients with …

Primary ciliary dyskinesia (PCD) is an inherited disorder characterized by recurrent infections
of the upper and lower respiratory tract, reduced fertility in males and situs inversus in …

… (median, 9 percent) and weight (median, 1.2 kg). Plasma osmolality was significantly increased
from 287 to 290 mmol kg−1, as well as increased phosphate and urea concentrations, …

Primary ciliary dyskinesia (PCD) is a genetically heterogeneous autosomal recessive disorder
characterized by recurrent infections of the respiratory tract associated with the abnormal …