Background: Lung clearance index (LCI), a measure of ventilation inhomogeneity derived
from the multiple-breath inert gas washout (MBW) technique, has been shown to detect …

Background Long-term benefits of newborn screening (NBS) for cystic fibrosis (CF) have
been established with respect to nutritional status, but effects on pulmonary health remain …

… Copyright © 2005, Hilary Wyatt and Tim Amyes. The right of Hilary Wyatt and Tim Amyes to
be identified as the authors of this work has been asserted in accordance with the Copyright, …

The clinical advantages of the newborn screening programme (NBS) in the UK are well
described in the literature. However, there has been little exploration of the psychosocial impact …

The tidal and raised volume rapid thoracoabdominal compression techniques are increasingly
used to detect diminished airway function in infancy. The aim of this study was to assess …

Incidence of pulmonary infection with nontuberculous mycobacteria (NTM) is increasing
among persons with cystic fibrosis (CF). We assessed prevalence and management in CF …

Background Nutrition is closely related to mortality and pulmonary and respiratory muscle
function in cystic fibrosis (CF) patients. We initially validated results from a bioelectrical …

With the advent of novel designer molecules for cystic fibrosis (CF) treatment, there is huge
need for early-life clinical trial outcomes, such as infant lung function (ILF). We investigated …

Cystic fibrosis is a common disease of the Caucasian population and is associated with
significant early mortality. We present a simple and rapid method for cystic fibrosis genotyping …

Introduction Cystic fibrosis is usually associated with chronic pulmonary sepsis and frequent
infective exacerbations. We report a very unusual cause of severe hypoxaemia in a woman …