| Present study | First author [ref.] | |||||
| Swanson [16] | Gupta [3] | Mager [4] | Pollak [5] | Cottin [17] | ||
| Patients n | 20 | 93 | 66 | 112 | 155 | 126 |
| Age yrs mean±sd (range) | 48±15 (25–86) | 40 (5–83) | 44 (13–77) | 45 (7–85) | 45 (7–77) | 43±17 (10–79) |
| Epistaxis | 5 | 49 | 74 | 90 | ||
| Telangiectasia | 15 | 86 | ||||
| Hepatic shunt | 10 | 4 | 10 | |||
| HHT % | 0 | 56 | 83 | 96 | 95 | 100 |
| Dyspnoea % | 50 | 53 | 56 | 59 | 56 | |
| Cyanosis % | 0 | 29 | 29 | 18 | ||
| Polycythaemia % | 5 | 13 | 27 | |||
| Migraine % | 30 | 38 | 46 | 16 | ||
| Haemoptysis % | 20 | 15 | 9 | 1 | 3 | 12 |
| Haemothorax % | 0 | 3 | 3 | 3 | ||
| CVA % | 20 | 29 | 42 | 14 | 33 | 16 |
| Brain abscess | 5 | 5 | 17 | 7 | 9 | 19 |
| Other abscess | 0 | 3 | 1 | 6 | 4 | |
| Asymptomatic | 30 | 16 | 34 | 16 | 15 | |
HHT: hereditary haemorrhagic telangiectasia; CVA: cerebral vascular accident.