UIP | Bronchiectasis | NSIP | Bronchiolitis | OP | DAD | Combined | Total | |
Patients | 57 | 31 | 16 | 11 | 5 | 5 | 19 | 144 |
Median survival yrs | 3.9 | 17 | 9.3 | 0.2 | 8.0 | 8.1 | ||
5-yr survival % | 36.6 | 87.1 | 93.8 | 88.9 | 60.0 | 20.0 | 59.2 | 60.1 |
10-yr survival % | 24.6 | 81.7 | 93.8 | 47.4 | 60.0 | 0.0 | 38.9 | 46.0 |
Total deaths | 45 (78.9) | 5 (16.1) | 2 (12.5) | 3 (27.3) | 2 (40.0) | 5 (100) | 9 (47.4) | 71 (49.3) |
Cause of death | ||||||||
Acute exacerbation of UIP | 15 | 0 | 0 | 0 | 0 | 0 | 4 | 19 |
Acute exacerbation of bronchiectasis | 0 | 2 | 0 | 0 | 0 | 0 | 1 | 3 |
Disease progression | 9 | 0 | 0 | 1 | 0 | 3 | 0 | 13 |
Pneumonia | 5 | 1 | 0 | 1 | 1 | 0 | 1 | 9 |
Other pulmonary infections | 3 | 1 | 0 | 0 | 0 | 0 | 0 | 4 |
Lung cancer | 5 | 1 | 0 | 0 | 0 | 0 | 0 | 6 |
Pneumothorax | 1 | 0 | 0 | 1 | 0 | 0 | 0 | 2 |
Drug-induced pneumonitis | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 1 |
Radiation pneumonitis# | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 1 |
Nonrespiratory disease | 5 | 0 | 2 | 0 | 1 | 2 | 3 | 13 |
Data are presented as n or n (%), unless otherwise indicated. UIP: usual interstitial pneumonia; NSIP: nonspecific interstitial pneumonia; OP: organising pneumonia; DAD: diffuse alveolar damage. #: due to irradiation for oesophageal cancer. p<0.001 (global log-rank test).