Table 3– Survival and causes of death in patients with lung disease directly associated with rheumatoid arthritis
UIPBronchiectasisNSIPBronchiolitisOPDADCombinedTotal
Patients573116115519144
Median survival yrs3.9179.30.28.08.1
5-yr survival %36.687.193.888.960.020.059.260.1
10-yr survival %24.681.793.847.460.00.038.946.0
Total deaths45 (78.9)5 (16.1)2 (12.5)3 (27.3)2 (40.0)5 (100)9 (47.4)71 (49.3)
Cause of death
 Acute exacerbation of UIP1500000419
 Acute exacerbation of bronchiectasis02000013
 Disease progression900103013
 Pneumonia51011019
 Other pulmonary infections31000004
 Lung cancer51000006
 Pneumothorax10010002
 Drug-induced pneumonitis10000001
 Radiation pneumonitis#10000001
 Nonrespiratory disease502012313
  • Data are presented as n or n (%), unless otherwise indicated. UIP: usual interstitial pneumonia; NSIP: nonspecific interstitial pneumonia; OP: organising pneumonia; DAD: diffuse alveolar damage. #: due to irradiation for oesophageal cancer. p<0.001 (global log-rank test).