Recommendations for pulmonary hypertension(PH) due to lung diseases
| Statement | Class# | Level¶ |
| Echocardiography is recommended as a screening tool for the assessment of PH due to lung diseases | I | C |
| RHC is recommended for a definite diagnosis of PH due to lung diseases | I | C |
| The optimal treatment of the underlying lung disease including long-term O2 therapy in patients with chronic hypoxaemia is recommended in patients with PH due to lung diseases | I | C |
| Patients with “out of proportion” PH due to lung diseases should be enrolled in RCTs targeting PAH-specific drugs | IIa | C |
| The use of PAH-specific drug therapy is not recommended in patients with PH due to lung diseases | III | C |
RHC: right heart catheterisation; RCT: randomised controlled trial; PAH: pulmonary arterial hypertension. #: class of recommendation; ¶: level of evidence.