Table 29—

Recommendations for pulmonary veno-occlusive disease

Referral of patients with PVOD to a transplant centre for evaluation is indicated as soon as the diagnosis is establishedIC
Patients with PVOD should be managed only in centres with extensive experience in PAH due to the risk of lung oedema after the initiation of PAH-specific drug therapyIIaC
  • PVOD: pulmonary veno-occlusive disease; PAH: pulmonary arterial hypertension. #: class of recommendation; : level of evidence.