Recommendations for pulmonary arterial hypertension(PAH) associated with portal hypertension
| Statement | Class# | Level¶ |
| Echocardiographic screening for the detection of PH is recommended in symptomatic patients with liver diseases and/or in candidates for liver transplantation | I | B |
| In patients with PAH associated with portal hypertension the same treatment algorithm as in patients with IPAH should be considered, taking into consideration comorbidities | IIa | C |
| Anticoagulation is not recommended in patients with increased risk of bleeding | III | C |
| Significant PAH is a contraindication to liver transplantation if P̄pa is ≥35 mmHg and/or PVR is ≥250 dynes·s−1·cm−5 | III | C |
PH: pulmonary hypertension; IPAH: idiopathic PAH; P̄pa: mean pulmonary arterial pressure; PVR: pulmonary vascular resistance. #: class of recommendation; ¶: level of evidence.