Table 13—

Recommendations for diagnostic strategy

Ventilation/perfusion lung scan is recommended in patients with unexplained PH to exclude CTEPHIC
Contrast CT angiography of the PA is indicated in the work-up of patients with CTEPHIC
Routine biochemistry, haematology, immunology and thyroid function tests are indicated in all patients with PAH, to identify the specific associated conditionIC
Abdominal ultrasound is indicated for the screening of portal hypertensionIC
High-resolution CT should be considered in all patients with PHIIaC
Conventional pulmonary angiography should be considered in the work-up of patients with CTEPHIIaC
Open or thoracoscopic lung biopsy is not recommended in patients with PAHIIIC
  • PH: pulmonary hypertension; CTEPH: chronic thromboembolic pulmonary hypertension; CT: computed tomography; PA: pulmonary artery; PAH: pulmonary arterial hypertension. #: class of recommendation; : level of evidence.