Diagnoses by participating centres
Diagnosis | All patients | Vienna | Prague | Homburg |
CTEPH | 433 | 202 | 54 | 177 |
Operable | 282 (65.9) | 117 (59.4) | 39 (72.2) | 130 (73.4) |
Inoperable | 146 (34.1) | 80 (40.6) | 15 (27.8) | 47 (26.6) |
Missing | 5 | 5 | 0 | 0 |
PEA performed | 248 (57.3) | 94 (46.5) | 39 (72.2) | 115 (65.0) |
PAH | 254 | 157 | 41 | 56 |
Idiopathic | 118 (46.5) | 79 (50.3) | 27 (65.9) | 12 (21.4) |
Familial | 4 (1.6) | 2 (1.3) | 0 | 2 (3.6) |
Associated with | ||||
CVD | 28 (11.0) | 12 (7.6) | 6 (14.6) | 10 (17.9) |
CHD | 13 (5.1) | 10 (6.4) | 0 | 3 (5.4) |
Eisenmenger | 27 (10.6 | 18 (11.5 | 3 (7.3) | 6 (10.7) |
Portal hypertension | 19 (7.5) | 13 (8.3) | 0 | 6 (10.7) |
HIV | 5 (2.0) | 4 (2.5) | 0 | 1 (1.8) |
Appetite suppressants | 10 (3.9) | 6 (3.8) | 1 (2.4) | 3 (5.4) |
Hereditary haemorrhagic teleangiectasia | 3 (1.1) | 3 (1.9) | 0 | 0 |
Other nonthromboembolic PH | 27 (10.6) | 10 (6.3) | 4 (9.8) | 13 (23.2) |
Data are presented as n or n (%). CTEPH: chronic thromboemolic pulmonary hypertension; PEA: pulmonary endarterectomy; PAH: pulmonary arterial hypertension; CVD: collagen vascular disease; CHD: congenital heart disease; nonthromboembolic PH: nonthromboembolic pre-capillary PAH (diagnostic categories: sarcoidosis, histiocytosis X, sleep apnoea, veno-occlusive disease and haemolytic anaemia).