Table 1—

Diagnoses by participating centres

DiagnosisAll patientsViennaPragueHomburg
CTEPH43320254177
 Operable282 (65.9)117 (59.4)39 (72.2)130 (73.4)
 Inoperable146 (34.1)80 (40.6)15 (27.8)47 (26.6)
 Missing5500
 PEA performed248 (57.3)94 (46.5)39 (72.2)115 (65.0)
PAH2541574156
 Idiopathic118 (46.5)79 (50.3)27 (65.9)12 (21.4)
 Familial4 (1.6)2 (1.3)02 (3.6)
 Associated with
  CVD28 (11.0)12 (7.6)6 (14.6)10 (17.9)
  CHD13 (5.1)10 (6.4)03 (5.4)
  Eisenmenger27 (10.618 (11.53 (7.3)6 (10.7)
  Portal hypertension19 (7.5)13 (8.3)06 (10.7)
  HIV5 (2.0)4 (2.5)01 (1.8)
  Appetite suppressants10 (3.9)6 (3.8)1 (2.4)3 (5.4)
  Hereditary haemorrhagic teleangiectasia3 (1.1)3 (1.9)00
Other nonthromboembolic PH27 (10.6)10 (6.3)4 (9.8)13 (23.2)
  • Data are presented as n or n (%). CTEPH: chronic thromboemolic pulmonary hypertension; PEA: pulmonary endarterectomy; PAH: pulmonary arterial hypertension; CVD: collagen vascular disease; CHD: congenital heart disease; nonthromboembolic PH: nonthromboembolic pre-capillary PAH (diagnostic categories: sarcoidosis, histiocytosis X, sleep apnoea, veno-occlusive disease and haemolytic anaemia).