Table 1—

Patient characteristics at baseline(BL) and at the second visit 1 yr later

MMDDMD
Subjects n6125
Age yrs#42.2±11.622.1±3.7
Males/females n42/1925/0
BMI kg·m−2 #25.8±6.217.3±5.4
Noninvasive mechanical ventilation n
 BL511
 Visit 22117
VC % pred
 BL63.4±16.921.9±9.1
 Visit 262.0±18.017.7±7.6*
SNIP cmH2O
 BL45.0±21.120.2±9.5
 Visit 248.9±22.216.3±9.0*
PI,max cmH2O
 BL43.8±20.024.2±9.7
 Visit 241.5±19.021.3±7.6*
  • Data are presented as mean±sd, unless otherwise stated. MMD: myotonic muscular dystrophy; DMD: Duchenne muscular dystrophy; BMI: body mass index; VC: vital capacity; % pred: % predicted; SNIP: sniff nasal inspiratory pressure; PI,max: maximal inspiratory pressure. #: determined at BL. *: p<0.05 versus BL (Wilcoxon test).