Haemodynamics at the time of diagnosis for patients in each subtype of pulmonary arterial hypertension(PAH)
| IPAH/FPAH | CTD | Congenital heart disease | Anorexigen | HIV | Portal hypertension | p-value | |
| mRAP mmHg | 11±7 | 11±6 | 10±7 | 13±5 | 14±5 | 12±7 | 0.17 |
| mPAP mmHg | 56±13 | 48±11 | 54±22 | 52±12 | 50±5 | 46±14 | <0.0001 |
| PCWP mmHg | 10±4 | 10±4 | 13±8 | 9±3 | 10±2 | 12±5 | <0.0001 |
| Cardiac index L·min−1·m−2 | 2±0.7 | 2.3±0.8 | 2.8±0.7 | 1.9±0.7 | 2.3±0.8 | 3.2±1.5 | <0.0001 |
| PA,O2 saturation | 57±11 | 57±11 | 66±14 | 54±13 | 54±9 | 62±13 | <0.0001 |
| PVR Woods unit | 14±6.8 | 11.1±5.9 | 13.2±11.4 | 13.5±7.1 | 10.3±3.3 | 7.4±5.3 | <0.0001 |
| Acute vasodilator responders | 5.4 | 2.3 | 12.5 | 0 | 0 | 0 | 0.12 |
Data are presented as mean±sd or %, unless otherwise stated. IPAH: idiopathic PAH; FPAH: familial PAH; CTD: connective tissue disease; mRAP: mean right atrial pressure; mPAP: mean pulmonary artery pressure; PCWP: pulmonary capillary wedge pressure; PA,O2: alveolar oxygen partial pressure; PVR: pulmonary vascular resistance.