Baseline haemodynamic data
Fen-PAH | IPAH | p-value | |
Right atrial pressure mmHg | 11±6 | 10±5 | ns |
Mean pulmonary artery pressure mmHg | 60±12 | 60±14 | ns |
Pulmonary artery occlusion pressure mmHg | 9±3 | 9±3 | ns |
Cardiac index L·min−1·m−2 | 2.2±0.6 | 2.3±0.7 | ns |
Indexed pulmonary vascular resistance U·m−2 | 30±11 | 29±12 | ns |
Proportion of responders at the acute vasodilator challenge % | 8.3 (4.0–16.2) | 12.1 (9.5–15.3) | ns |
Data are presented as mean±sd and % (95% confidence interval) unless otherwise stated. Fen-PAH: fenfluramine-associated pulmonary arterial hypertension (PAH); IPAH: idiopathic PAH; ns: nonsignificant.