Baseline clinical characteristics of patients by aetiology of pulmonary arterial hypertension(PAH)
| Clinical Data | IPAH/FPAH | CTD | Congenital heart disease | Anorexigen | HIV | Portal hypertension | p-value |
| Age yrs | 45±14 | 55±15 | 42±12 | 52±11 | 40±4 | 49±9 | <0.0001 |
| Female | 75 | 87 | 68 | 100 | 13 | 70 | <0.0001 |
| WHO functional class | |||||||
| Mean | 3.0±0.9 | 3.2±0.7 | 2.8±0.9 | 3.1±0.7 | 2.7±0.8 | 2.9±0.9 | <0.007 |
| Class I | 7 | 3 | 10 | 0 | 0 | 7 | |
| Class II | 13 | 9 | 21 | 19 | 43 | 22 | |
| Class III | 49 | 49 | 45 | 56 | 43 | 49 | |
| Class IV | 31 | 39 | 24 | 25 | 14 | 22 | |
| Exercise capacity METs | 3.7±3.1 | 3.1±2.7 | 3.9±2.9 | 3.6±3.2 | 3.3±3.7 | 3.5±3.0 | 0.199 |
Data are presented as mean±sd or %, unless otherwise stated. IPAH: idiopathic PAH; FPAH: familial PAH; CTD: connective tissue disease; WHO: World Health Organization; METs: metabolic equivalents.