Table 2—

Prevalence and incidence of pulmonary arterial hypertension and its subtypes from three sources#

TotalIPHCTD-PHCHD-PH
Prevalence
 French156.52.31.7
 SMR52251512
 SPVU269107
Incidence
 French2.41.00.40.3
 SMR7.13.32.11.7
 SPVU7.62.62.82.2
  • Data are presented as cases per million population and annual cases per million population for prevalence and incidence, respectively. IPH: idiopathic pulmonary hypertension (PH); CTD-PH: connective tissue disease-associated PH; CHD-PH: congenital heart disease-associated PH; SMR: Scottish Morbidity Record; SPVU: Scottish Pulmonary Vascular Unit. #: SMR, SPVU database and the French national registry.