Table 1—

Pulmonary arterial hypertension history

Subjects n860
IPAH412 (48)
IPAH associated with
  Congenital systemic to pulmonary shunts177 (21)
  Diffuse cutaneous systemic sclerosis72 (8)
  Thromboembolic disease49 (6)
  Portopulmonary hypertension43 (5)
  Systemic lupus erythematosus35 (4)
  Limited cutaneous systemic sclerosis28 (3)
  Mixed connective tissue disease27 (3)
  HIV13 (2)
  Overlap syndrome4 (<1)
Months since diagnosis42±74
  No806 (93)
  Yes13 (2)
  Unknown41 (5)
NYHA functional class at baseline
  II128 (15)
  III654 (76)
  IV78 (9)
Months at baseline NYHA functional class15±31
  • Data are presented as n (%) or mean±sd, unless otherwise stated. IPAH: idiopathic pulmonary arterial hypertension; NYHA: New York Heart Association.