Table 1—

Baseline characteristics of patients

IPAHPAH-SSDp-value
Subjects n1312
Age yrs60±852±130.06
Race white10 (77)8 (75)ns
Sex female12 (92)12 (100)ns
NYHA FC at diagnosis I/II versus III/IV3/102/10ns
6MWD m270±147318±76ns
RAP mmHg14±512±6ns
mPpa mmHg57±1253±10ns
CI L·min−1·m−22.3±1.02.1±0.4ns
PVR Wood unit13±511±4ns
Ppcw mmHg12±312±3ns
Warfarin use9 (69)6 (50)ns
Calcium channel blocker use1 (8)3 (25)ns
Digoxin use2 (15)1 (8)ns
  • Data are presented as mean±sd or n (%), unless otherwise stated. IPAH: idiopathic pulmonary arterial hypertension (PAH); PAH-SSD: scleroderma-associated PAH; NYHA: New York Heart Association; FC: functional class; 6MWD: 6-min walk distance; RAP: right atrial pressure; mPpa: mean pulmonary arterial pressure; CI: cardiac index; PVR: pulmonary vascular resistance; Ppcw: pulmonary capillary wedge pressure; ns: nonsignificant.