IPAH patient No. | Sex | Age yrs | NYHA baseline | 6-MWD m | mPAP mmHg | PAWP mmHg | TPR IU·m−2 | CI L·min−1·m−2 | Pa,O2 mmHg | DL,CO/VA% pred | Alveolar cell·mL−1 | Golde score |
1 | F | 43 | III | 360 | 57 | 10 | 24 | 2.4 | 94 | 57 | 206000 | 0 |
2 | M | 54 | III | 350 | 58 | 12 | 27 | 2.1 | 68 | 90 | 592000 | 30 |
3 | F | 64 | III | 400 | 47 | 6 | 24 | 2 | 69 | 71 | 99000 | 16 |
4 | F | 52 | IV | 230 | 72 | 7 | 31 | 2.3 | 61 | 76 | 255000 | 5 |
5 | F | 40 | II | 360 | 54 | 6 | 15 | 3.5 | 87 | 58 | 160000 | 0 |
6 | M | 31 | IV | 380 | 56 | 7 | 25 | 2.2 | 78 | 83 | 122000 | 0 |
7 | F | 33 | III | 255 | 75 | 9 | 50 | 1.5 | 50 | 45 | 0 | |
8 | F | 43 | III | 420 | 66 | 8 | 25 | 2.6 | 93 | 57 | 109000 | 0 |
9 | F | 48 | III | 420 | 39 | 6 | 12 | 3.2 | 88 | 51 | 73000 | 0 |
10 | M | 44 | II | 535 | 53 | 15 | 17 | 3 | 77 | 36 | 328000 | 0 |
11 | F | 31 | III | 380 | 65 | 11 | 29 | 2.2 | 90 | 59 | 99000 | 0 |
Mean±sd | 44±10 | 372±82 | 58±10 | 9±3 | 25±10 | 2.5±0.6 | 78±14 | 62±16 | 204300±158200 | 4±10 |
NYHA: New York Heart Association; 6-MWD: 6-min walk distance; mPAP: mean pulmonary artery pressure; PAWP: pulmonary artery wedge pressure; TPR: total pulmonary resistance; CI: cardiac index; Pa,O2: arterial oxygen pressure; DL,CO/VA % pred: carbon monoxide diffusing capacity/alveolar volume percentage predicted; F: female; M: male. 1 mmHg = 0.133 kPa.