Table 2—

Comparison between A/A and O/O subjects matched for sex, age and cystic fibrosis transmembrane regulator (CFTR) genotype

TripletMBL-2 haplotypeSexCFTRAge yrsFEV1 %FVC %P. aeruginosa
1A/AMΔ/−2060.380.1N
A/A2075.595.6Y
O/O2054.965.9Y
2A/AMΔ/−4236.669.5Y
A/A4286.1104Y
O/O4218.538.7Y
3A/AFΔ/−2497.8100.4Y
A/A2560.892.4Y
O/O2478.092.8Y
4A/AFΔ/Δ2948.077.5Y
A/A2950.458.5Y
O/O2937.354.6Y
5A/AMΔ/Δ2237.872.3Y
A/A2262.874.6Y
O/O2253.574.0Y
6A/AFΔ/Δ21104.4100.7Y
A/A2199.799.8Y
O/O2161.674.9Y
7A/AMΔ/−3739.369.0Y
A/A3920.763.4Y
O/O3829.151.5Y
8A/AFΔ/Δ3233.361.6Y
O/O3640.356.4Y
9A/AMΔ/Δ4490.6114.5Y
O/O4351.172.1N
10A/AM−/−1987.292.5Y
A/A20110.396.2N
O/O1950.653.4Y
11A/AM−/−5476.382.5Y
O/O5148.578.8N
Mean A/A30.7±2.366.1±5.784.7±3.4
Mean O/O31.4±3.4#47.6±4.864.8±4.7+
  • MBL: mannose-binding lectin; FEV1: forced expiratory volume in one second; FVC: forced vital capacity; P. aeruginosa: Pseudomonas aeruginosa; M: male; F: female; Δ: ΔF508; −: other mutation; N: no; Y: yes. #: p=0.9; : p=0.02; +: p<0.01, compared with matched A/A counterparts