Triplet | MBL-2 haplotype | Sex | CFTR | Age yrs | FEV1 % | FVC % | P. aeruginosa |
1 | A/A | M | Δ/− | 20 | 60.3 | 80.1 | N |
A/A | 20 | 75.5 | 95.6 | Y | |||
O/O | 20 | 54.9 | 65.9 | Y | |||
2 | A/A | M | Δ/− | 42 | 36.6 | 69.5 | Y |
A/A | 42 | 86.1 | 104 | Y | |||
O/O | 42 | 18.5 | 38.7 | Y | |||
3 | A/A | F | Δ/− | 24 | 97.8 | 100.4 | Y |
A/A | 25 | 60.8 | 92.4 | Y | |||
O/O | 24 | 78.0 | 92.8 | Y | |||
4 | A/A | F | Δ/Δ | 29 | 48.0 | 77.5 | Y |
A/A | 29 | 50.4 | 58.5 | Y | |||
O/O | 29 | 37.3 | 54.6 | Y | |||
5 | A/A | M | Δ/Δ | 22 | 37.8 | 72.3 | Y |
A/A | 22 | 62.8 | 74.6 | Y | |||
O/O | 22 | 53.5 | 74.0 | Y | |||
6 | A/A | F | Δ/Δ | 21 | 104.4 | 100.7 | Y |
A/A | 21 | 99.7 | 99.8 | Y | |||
O/O | 21 | 61.6 | 74.9 | Y | |||
7 | A/A | M | Δ/− | 37 | 39.3 | 69.0 | Y |
A/A | 39 | 20.7 | 63.4 | Y | |||
O/O | 38 | 29.1 | 51.5 | Y | |||
8 | A/A | F | Δ/Δ | 32 | 33.3 | 61.6 | Y |
O/O | 36 | 40.3 | 56.4 | Y | |||
9 | A/A | M | Δ/Δ | 44 | 90.6 | 114.5 | Y |
O/O | 43 | 51.1 | 72.1 | N | |||
10 | A/A | M | −/− | 19 | 87.2 | 92.5 | Y |
A/A | 20 | 110.3 | 96.2 | N | |||
O/O | 19 | 50.6 | 53.4 | Y | |||
11 | A/A | M | −/− | 54 | 76.3 | 82.5 | Y |
O/O | 51 | 48.5 | 78.8 | N | |||
Mean A/A | 30.7±2.3 | 66.1±5.7 | 84.7±3.4 | ||||
Mean O/O | 31.4±3.4# | 47.6±4.8¶ | 64.8±4.7+ |
MBL: mannose-binding lectin; FEV1: forced expiratory volume in one second; FVC: forced vital capacity; P. aeruginosa: Pseudomonas aeruginosa; M: male; F: female; Δ: ΔF508; −: other mutation; N: no; Y: yes. #: p=0.9; ¶: p=0.02; +: p<0.01, compared with matched A/A counterparts