Subject | Sex | Age yrs | FEV1 % | FVC % | Microbiology | Genotype |
1 | F | 20 | 32 | 49 | PA (mt, mc) | ΔF508/ΔF508 |
2 | F | 18 | 61 | 83 | PA (mt, mc), SA | NA |
3 | M | 20 | 34 | 77 | PA (mt, mc) | NA |
4 | M | 21 | 31 | 48 | PA (mt, mc), CA | NA |
5 | M | 37 | 45 | 74 | PA (mc) | ΔF508/ΔF508 |
6 | M | 32 | 28 | 56 | PA (mt, mc) | ΔF508/NI |
7 | M | 19 | 21 | 33 | NI | ΔF508/ΔF508 |
8 | F | 40 | 36 | 65 | PA (mt, mc) | ΔF508/ΔF508 |
9 | M | 29 | 32 | 69 | PA (mc), CA | ΔF508/ΔF508 |
10 | M | 27 | 30 | 61 | PA (mt, mc) | ΔF508/ΔF508 |
11 | M | 23 | 57 | 82 | PA (mc) | NI |
12 | M | 26 | 43 | 84 | PA (mc), CA | ΔF508/ΔF508 |
13 | M | 29 | 24 | 50 | PA (mt, mc), MRSA | ΔF508/G551D |
14 | M | 28 | 37 | 50 | PA (mt, mc), MRSA | ΔF508/NI |
15 | M | 28 | 62 | 108 | PA (mt, mc), SA | ΔF508/G551D |
16 | M | 34 | 29 | 50 | PA (mc) | ΔF508/G551D |
17 | F | 25 | 35 | 48 | PA (mt, mc) | NA |
18 | M | 20 | 32 | 54 | PA (mt, mc), CA | NA |
19 | F | 21 | 47 | 69 | PA (mt, mc) | NA |
Median | 5F/14M | 26.5 (18–40) | 33 (21–62) | 55 (33–108) |
Data are presented as n and median (range) unless otherwise stated
FEV1: forced expiratory volume in one second
FVC: forced vital capacity
F: female
M: male
PA: Pseudomonas aeruginosa
mt: matt
mc: mucoid
SA: Staphylococcus aureus
CA: Candida albicans
MRSA: methicillin-resistant S. aureus
NA: not available
NI: not identifiable