Table 1—

Demographics of acute cystic fibrosis patients

SubjectSexAge yrsFEV1 %FVC %MicrobiologyGenotype
1F203249PA (mt, mc)ΔF508/ΔF508
2F186183PA (mt, mc), SANA
3M203477PA (mt, mc)NA
4M213148PA (mt, mc), CANA
5M374574PA (mc)ΔF508/ΔF508
6M322856PA (mt, mc)ΔF508/NI
7M192133NIΔF508/ΔF508
8F403665PA (mt, mc)ΔF508/ΔF508
9M293269PA (mc), CAΔF508/ΔF508
10M273061PA (mt, mc)ΔF508/ΔF508
11M235782PA (mc)NI
12M264384PA (mc), CAΔF508/ΔF508
13M292450PA (mt, mc), MRSAΔF508/G551D
14M283750PA (mt, mc), MRSAΔF508/NI
15M2862108PA (mt, mc), SAΔF508/G551D
16M342950PA (mc)ΔF508/G551D
17F253548PA (mt, mc)NA
18M203254PA (mt, mc), CANA
19F214769PA (mt, mc)NA
Median5F/14M26.5 (18–40)33 (21–62)55 (33–108)
  • Data are presented as n and median (range) unless otherwise stated

  • FEV1: forced expiratory volume in one second

  • FVC: forced vital capacity

  • F: female

  • M: male

  • PA: Pseudomonas aeruginosa

  • mt: matt

  • mc: mucoid

  • SA: Staphylococcus aureus

  • CA: Candida albicans

  • MRSA: methicillin-resistant S. aureus

  • NA: not available

  • NI: not identifiable