Long-term improvement after whole lung lavage#
| Baseline | Last evaluation | p‐value | |
| TLC % pred | 65±21 | 73±29 | ns |
| FVC % pred | 62±13 | 81±13 | <0.001 |
| DL,CO % pred | 44±16 | 75±19 | <0.005 |
| Pa,O2 mmHg | 55±12 | 78±11 | <0.0005 |
| PA‐a,O2 mmHg | 52±13 | 27±11 | <0.0001 |
| Treadmill distance m | 209±156 | 626±264 | <0.005 |
Data are presented as mean±sd (n=11)
TLC: total lung capacity
FVC: forced vital capacity
DL,CO: diffusing capacity of the lung for carbon monoxide
Pa,O2: arterial oxygen tension
PA‐a,O2: alveolar to arterial oxygen tension difference
% pred: percentage of the predicted value
ns: nonsignificant
#: at median of 5±2 yrs
(1 mmHg=0.133 kPa.)