Table 1—

Cardiac and pulmonary function measurements

Absolute valuePercentage of predicted value#
LVEF %31.2±9.8
FEV1 L2.70±0.4877.3±7.8
FVC L3.54±0.5578.6±6.8
FEV1/FVC %75.6±4.0
TLC L6.11±0.9289.0±14.5
RV L2.46±0.56103.1±29.2
DL,CO mL·min−1·mmHg−122.27±8.081.0±25.0
PI,max cmH2O94±2187.1±18.0
MVV L·min−1109.1±21.082.2±11.4
  • Data are presented as mean±sd

  • LVEF: left ventricular ejection fraction

  • FEV1: forced expiratory volume in one second

  • FVC: forced vital capacity

  • TLC: total lung capacity

  • RV: residual volume

  • DL,CO: diffusing capacity of the lung for carbon monoxide

  • PI,max: maximal inspiratory pressure

  • MVV: maximum voluntary ventilation

  • #: from 13–16