Table 2—

Course of neuromuscular and neurological disease

Rapidly progressiveVariable progressionSlowly progressive or nonprogressive
Motor neurone disease/ALSLimb girdle MDPrevious poliomyelitis
DMD (in teenage years)MyopathiesFacio scapulo humeral MD
NemalineType III SMA
MetabolicCentral hypoventilation
Merosin negative congenital muscular dystrophySpinal cord injury
  • ALS: amyotrophic lateral sclerosis

  • DMD: Duchenne muscular dystrophy

  • SMA: spinal muscular abrophy

  • MD: muscular dystrophy