Patient number | Age yrs | Study number | Shwachman's score 5 | FEV1 % | FVC % | FEF25–75 % | VT mL | RR·min−1 |
1 | 11 | 1a | 83 | 87.3 | 100.1 | 75.5 | 790 | 14 |
1b | 83 | 69.5 | 101.6 | 40.7 | 550 | 16 | ||
2 | 9 | 2a | 68 | 50.3 | 85.6 | 19.2 | ND | ND |
2b | 83 | 68.7 | 99.1 | 30.3 | 440 | 21 | ||
3 | 31 | 3a | ND | 28.9 | 60.5 | 10.5 | 980 | 11 |
3b | ND | 32.0 | 68.6 | 11.1 | 1260 | 11 | ||
3c | ND | 28.1 | 68.0 | 9.7 | ND | ND | ||
4 | 10 | 4a | 82 | 82.5 | 100.6 | 57.9 | 730 | 10 |
4b | 82 | 65.7 | 88.1 | 36.1 | ND | ND | ||
5 | 8 | 5a | 89 | 82.5 | 96.2 | 67.5 | 600 | 11 |
5b | 83 | 83.6 | 104.9 | 55.7 | 360 | 12 | ||
6 | 8 | 6a | 97 | 99.9 | 106.5 | 88.8 | 380 | 13 |
7 | 17 | 7a | 58 | 24.6 | 34.4 | 9.3 | ND | 15 |
7b | 55 | 21.5 | 26.0 | 13.2 | 370 | 12 | ||
Median | 10 | 83 | 68.7 | 96.2 | 36.1 | 600 | 12.5 | |
Mean | 13.4 | 78.5 | 58.9 | 81.4 | 37.5 | 690 | 13.5 | |
95%CI of the mean | 69.9–87.1 | 43.2–74.7 | 66.3–96.6 | 21.8–53.3 | 480–910 | 11.5–15.5 |
FEV1: force expiratory volume in one second
FVC: force vital capacity
FEF25–75 %: forced mid-expiratory flow
VT: tial volume
RR: respiratory rate
ND: not determined
CI: confidence interval
FEV1 and FVC and FEF25–75 are expressed as the percentage of the predicted values