TABLE 2

Individual progressive fibrosing interstitial lung disease (PF-ILD) criteria met within 24 months of ILD diagnosis

First PF-ILD criterion met within 24 months of ILD diagnosis
Relative FVC decline ≥10%675 (49)
Relative FVC decline 5–9% with worsening respiratory symptoms166 (12)
Relative FVC decline 5–9% with worsening fibrosis on HRCT113 (8)
Relative FVC decline <5% with both symptom and radiographic progression352 (26)
Lung transplantation9 (1)
Death#61 (4)
Total1376 (100)

Data are presented as n (%). FVC: forced vital capacity; HRCT: high-resolution computed tomography. #: these patients died without meeting any of the other criteria.