Baseline and admission characteristics of the participants (n=15)
| Characteristics | |
| Baseline | |
| Age years | 14 (13.0–16.5) |
| Male sex | 5 (33.3) |
| Height cm | 153 (148–163) |
| Weight kg | 43.4 (38.2–48.6) |
| Pancreatic insufficient | 12 (80.0) |
| CF liver disease | 1 (6.7) |
| Number of admissions in previous 18 months; mean (range) | 1.2 (0–5) |
| Baseline FEV1 % pred (best in past 6 months) | 85.0 (61.0–93.0) |
| Admission | |
| Akron pulmonary exacerbation score | 11.0 (8.0–14.0) |
| Likert wellness score (1–10 scale) | 7 (5–7) |
| Relative drop in FEV1 % pred from baseline on admission | −18.0 (−8.0– −31.0) |
| FEV1 % pred | 62.9±13.9 |
| LCI (sitting) | 15.1±2.4 |
| BMI percentile | 22 (4–39) |
| Positive sputum microbiology at admission | |
| Methicillin-sensitive Staphylococcus aureus | 7 (46.7) |
| Pseudomonas aeruginosa | 4 (26.7) |
| Achromobacter spp. | 3 (20.0) |
| Aspergillus spp. | 2 (13.3) |
| Mycobacterium abscessus | 2 (13.3) |
| Other | 5 (33.3) |
Data are presented as median (IQR), n (%) or mean±sd, unless otherwise stated. CF: cystic fibrosis; FEV1: forced expiratory volume in 1 s; LCI: lung clearance index; BMI: body mass index.