Main characteristics of the patients at diagnosis (n=35)
| Characteristics | Result |
| Age at diagnosis years | 53.1 (28.0–80.6) |
| Male | 21 (60.0) |
| ILD cases per family | 3 (1–5) |
| Aero-contaminant exposure | |
| Ever smoker | 25 (71.4) |
| Fibrogenic exposure | 11 (31.4) |
| Smoking or fibrogenic exposure | 29 (82.9) |
| PFTs | |
| FVC % predicted | 75 (36–128) |
| DLCO % predicted | 61 (28–112) |
| Computed tomography pattern (n=31) | |
| Typical or probable UIP | 25 (80.6) |
| Indeterminate or inconsistent with UIP | 6 (19.3) |
| Histological pattern (n=10) | |
| Definite or probable UIP | 7 |
| NSIP | 1 |
| NSIP + DIP | 1 |
| PC | 1 |
| Multidisciplinary diagnosis | |
| IPF# | 20 (57.1) |
| RA–ILD | 4 (11.4) |
| IPAF | 3 (8.6) |
| UnF | 4 (11.4) |
| Chronic HP | 2 (5.7) |
| Sarcoidosis | 1 (2.9) |
| PC | 1 (2.9) |
Data are presented as n, n (%) or median (range). ILD: interstitial lung disease; PFT: pulmonary function test; FVC: forced vital capacity; DLCO: diffusing capacity of the lung for carbon monoxide; UIP: usual interstitial pneumonia; NSIP: nonspecific interstitial pneumonia; DIP: desquamative interstitial pneumonia; PC: pneumoconiosis; IPF: idiopathic pulmonary fibrosis; RA: rheumatoid arthritis; IPAF: interstitial pneumonia with autoimmune features; UnF: unclassifiable fibrosis; HP: hypersensitivity pneumonitis. #: IPF, or probable IPF or possible IPF diagnosis based on CT scan and histology. Patients with probable UIP on CT scan without histology, but with a working diagnosis of IPF after multidisciplinary discussion, are classified as IPF.