TABLE 1

Criteria favouring group 1 versus group 3 pulmonary hypertension (PH)#

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PAH: pulmonary arterial hypertension; FEV1: forced expiratory volume in 1 s; COPD: chronic obstructive pulmonary disease; FVC: forced vital capacity; IPF: idiopathic pulmonary fibrosis; CT: computed tomography; BMPR2: bone morphogenetic protein receptor type 2; CO: cardiac output; VO2: oxygen uptake; PaCO2: arterial carbon dioxide tension. #: group 2 and 4 patients are excluded based on the diagnostic criteria of these groups; : parenchymal changes linked to pulmonary veno-occlusive disease may be discriminated from those associated with diffuse parenchymal lung diseases; +: features of a limited circulatory reserve may be noted in severe COPD-PH and severe IPF-PH.