TABLE 4

Developmental lung disorders associated with pulmonary hypertension

Bronchopulmonary dysplasia
Congenital diaphragmatic hernia
Down syndrome
Alveolar capillary dysplasia with “misalignment of veins” (FOXF1)
Lung hypoplasia, acinar dysplasia
Surfactant protein abnormalities
 Surfactant protein B deficiency
 Surfactant protein C deficiency
 ABCA3
TTF1/NKX2-1
TBX4
Pulmonary interstitial glycogenesis
Pulmonary alveolar proteinosis
Pulmonary lymphangiectasia