Continuous positive airway pressure | Long-term oxygen therapy | Home mechanical ventilation | |
Patients | 7737 | 4750 | 1446 |
Neuromuscular disorders (nonspecific) | 4713 (60.9) | 2500 (52.6) | 769 (53.2) |
Myasthenia gravis | 1255 (16.2) | 722 (15.2) | 149 (10.3) |
Multiple sclerosis | 1051 (13.6) | 652 (13.7) | 124 (8.6) |
Muscular dystrophy | 334 (4.3) | 332 (7) | 245 (16.9) |
Cerebral palsy | 180 (2.3) | 170 (3.6) | 34 (2.4) |
Spina bifida | 95 (1.2) | 65 (1.4) | 36 (2.5) |
Neuropathy | 46 (0.6) | 84 (1.8) | 20 (1.4) |
Guillain–Barré syndrome | 35 (0.5) | 44 (0.9) | 16 (1.1) |
Metabolic disorders | 28 (0.4) | 99 (2.1) | <6 (<0.4) |
ALS/MND | <6 (<0.1) | 80 (1.7) | 53 (3.6) |
SMA | 0 | <6 (<0.1) | <6 (<0.4) |
Post-polio syndrome | 0 | 0 | 0 |
Comorbidities | |||
COPD | 964 (12.5) | 1792 (37.7) | 283 (19.6) |
CHF | 248 (3.2) | 865 (18.2) | 92 (6.4) |
Data are presented as n or n (%). ALS: amyotrophic lateral sclerosis; MND: motor neurone disease; SMA: spinal muscular atrophy; COPD: chronic obstructive pulmonary disease; CHF: congestive heart failure.