TABLE 3

Diagnosis of patients receiving home respiratory support

Continuous positive airway pressureLong-term oxygen therapyHome mechanical ventilation
Patients773747501446
Neuromuscular disorders (nonspecific)4713 (60.9)2500 (52.6)769 (53.2)
Myasthenia gravis1255 (16.2)722 (15.2)149 (10.3)
Multiple sclerosis1051 (13.6)652 (13.7)124 (8.6)
Muscular dystrophy334 (4.3)332 (7)245 (16.9)
Cerebral palsy180 (2.3)170 (3.6)34 (2.4)
Spina bifida95 (1.2)65 (1.4)36 (2.5)
Neuropathy46 (0.6)84 (1.8)20 (1.4)
Guillain–Barré syndrome35 (0.5)44 (0.9)16 (1.1)
Metabolic disorders28 (0.4)99 (2.1)<6 (<0.4)
ALS/MND<6 (<0.1)80 (1.7)53 (3.6)
SMA0<6 (<0.1)<6 (<0.4)
Post-polio syndrome000
Comorbidities
 COPD964 (12.5)1792 (37.7)283 (19.6)
 CHF248 (3.2)865 (18.2)92 (6.4)

Data are presented as n or n (%). ALS: amyotrophic lateral sclerosis; MND: motor neurone disease; SMA: spinal muscular atrophy; COPD: chronic obstructive pulmonary disease; CHF: congestive heart failure.