TABLE 1

Clinical characteristics of patients with cystic fibrosis

Subjects35
Visits39
Age years
 Median (IQR)27.7 (23.8–30.8)
 Range19.1–59.0
Male/female23/12
BMI kg·m−2
 Median (IQR)19.8 (18.9–21.4)
 Range16.3– 27.7
FEV1 % pred
 Median (IQR)53.3 (38.7–68.1)
 Range18.0–114.8
FRCpleth % pred#
 Median (IQR)140.4 (113.8–169.4)
 Range89.6–212.4
CFTR genotype
 F508del/F508del13/35 (37.1)
 F508del/other19/35 (54.3)
 Other/other3/35 (8.6)
Pseudomonas infection
 Negative13/39 (33.3)
 Intermittent3/39 (7.7)
 Chronic23/39 (59.0)
Pancreatic insufficiency30/35 (83.3)

Data are presented as n or n (%), unless otherwise stated. IQR: interquartile range; BMI: body mass index; FEV1: forced expiratory volume in 1 s; FRCpleth: plethysmographic functional residual capacity; CFTR: cystic fibrosis transmembrane conductance regulator. #: available in 28 of 39 visits.