TABLE 1

Case presentation

DateDecember 2013March 2014December 2014 to September 2015December 2016
EventsPregnancy
TreatmentNoneAmlodipine 20 mg once dailyAmlodipine 20 mg once dailySildenafil 20 mg three times daily, bosentan 125 mg twice daily, amlodipine 20 mg once daily
mPAP mmHg522856
mPAP with NO mmHg272151
CO L·min−13.95.13.8
CI L·min−1·m−22.53.32.4
PVR Wood units11.53.912.1
RV size and functionSeverely dilated, mildly impaired systolic functionNormal size, normal systolic functionModerate-severely dilated, severely impaired function
BNP pg·mL−160771775

mPAP: mean pulmonary arterial pressure; CO: cardiac output; CI: cardiac index; PVR: pulmonary vascular resistance; RV: right ventricular; BNP: brain natriuretic peptide.