TABLE 2

Crude prevalence and incidence of interstitial lung diseases (ILDs) in Seine-Saint-Denis (reviewed cases)

ILD casesPopulation >15 years of age#
Subjects nPrevalence per 100000Subjects nIncidence per 100000 per year
All identified cases117097.923219.4
Reviewed cases84871.021918.3
ILDs of known cause26021.8776.5
  CTDs/vasculitis14512.1393.3
  Pneumoconioses423.590.8
  Drug-induced ILDs312.6141.2
  HP282.3110.9
  Radiation-induced pneumonitis70.610.1
  Others70.620.3§
 IIPs14512.14524.4
  IPF988.2332.8
  NSIP201.7100.8
  Desquamative interstitial pneumonia100.830.3
  Organising pneumonia90.810.1
  Unclassified (despite SLB)60.550.4
  RBILD20.200.0
  LIP00.000.0
 Sarcoidosis36130.2584.9
 Particular ILDs221.8100.8
  LAM90.840.3
  CIEP50.410.1
  PLCH40.320.2
  PAP20.210.1
  Others+20.220.1
 Undetermined diagnosis605.0221.8
  Differential diagnosis between IPF and NSIP342.9131.1

CTDs: connective tissue diseases; HP: hypersensitivity pneumonitis; IIPs: idiopathic interstitial pneumonias; IPF: idiopathic pulmonary fibrosis; NSIP: nonspecific interstitial pneumonia; SLB: surgical lung biopsy; RBILD: respiratory bronchiolitis with ILD; LIP: lymphoid interstitial pneumonia; LAM: lymphangioleiomyomatosis; CIEP: chronic idiopathic eosinophilic pneumonia; PLCH: pulmonary Langerhans’ cell histiocytosis; PAP: pulmonary alveolar proteinosis. #: 1 194 601 inhabitants; : including chronic inflammatory colitis (n=4), amyloidosis (n=1), immunoglobulin G4 syndrome (n=1) and progeria (n=1); +: including alveolar microlithiasis (n=1) and Erdheim Chester's disease (n=1).