TABLE 3

Available data from different modules of the standardised dataset of 3013 primary ciliary dyskinesia (PCD) patients in the international PCD cohort (iPCD Cohort) (April 2016)

Type of dataPatients
General information3013 (100)
Diagnostics3013 (100)
 nNO1021 (33)
 TEM1913 (62)
 VM1088 (35)
 Genetics276 (9)
Baseline characteristics#2286 (74)
Growth1609 (53)
Lung function1042 (34)
Clinical manifestations1352 (44)
Therapy843 (27)
Microbiology732 (24)
Imaging526 (17)
Neonatal period1179 (38)
  • Data are presented as n (%). nNO: nasal nitric oxide; TEM: transmission electron microscopy; VM: light or high-frequency video microscopy. #: mainly data on situs anomalies and congenital heart disease.