TABLE 2

Interstitial pneumonia with autoimmune-features (IPAF) domains met by initial diagnosis

Domains metIPAF cohortInitial diagnosis
NSIP/COPIPFUCTD-ILDUnclassifiable
Subjects1449497214
Clinical and serological21 (14.6)0 (0)3 (6.1)17 (23.6)1 (7.1)
Clinical and morphological12 (8.3)2 (22.2)0 (0)6 (8.3)4 (28.6)
Serological and morphological73 (50.7)7 (77.8)43 (87.8)16 (22.2)7 (50)
All three domains38 (26.4)0 (0)3 (6.1)33 (45.8)2 (14.3)
  • Data are presented as n or n (%). NSIP: nonspecific interstitial pneumonia; COP: crytogenic organising pneumonia; IPF: idiopathic pulmonary fibrosis; UCTD: undifferentiated connective tissue disease; ILD: interstitial lung disease.