Patients | PAVM screening# | PAVM follow-up¶ | Increase in PAVM | Embolisation | |
Total | 200 | 37+ | 37 | 21 | 14 |
RLS increase | |||||
No RLS to grade 1 | 22 | 0 | NA | NA | NA |
Grade 1 to grade 2 | 10 | 5 | 5+ | 5 | 3 |
Grade 2 to grade 3 | 4 | 3 | 4 | 4 | 3 |
RLS decrease | |||||
Grade 1 to no RLS | 5 | 0 | NA | NA | NA |
Grade 2 to grade 1 | 8 | 0 | NA | NA | NA |
Grade 3 to grade 2 | 2 | 2 | 2 | 0 | 0 |
RLS no change | |||||
No RLS | 65 | 0 | NA | NA | NA |
Grade 1 | 45 | 3 | NA | NA | NA |
Grade 2 | 22 | 9 | 9 | 2 | 2 |
Grade 3 | 17 | 15 | 17 | 10 | 6 |
Data are presented as n. Subgroups are stratified according to pulmonary right-to-left shunt (RLS) grade and change during follow-up. Increase in PAVM is defined as increase of feeding artery of largest PAVM and/or presence of new PAVMs. NA: not applicable. #: chest CT advised in all patients; ¶: chest CT advised if pulmonary RLS grade ≥2; +: chest CT performed in eight patients.