Domains met | IPAF cohort | Initial diagnosis | |||
NSIP/COP | IPF | UCTD-ILD | Unclassifiable | ||
Subjects | 144 | 9 | 49 | 72 | 14 |
Clinical and serological | 21 (14.6) | 0 (0) | 3 (6.1) | 17 (23.6) | 1 (7.1) |
Clinical and morphological | 12 (8.3) | 2 (22.2) | 0 (0) | 6 (8.3) | 4 (28.6) |
Serological and morphological | 73 (50.7) | 7 (77.8) | 43 (87.8) | 16 (22.2) | 7 (50) |
All three domains | 38 (26.4) | 0 (0) | 3 (6.1) | 33 (45.8) | 2 (14.3) |
Data are presented as n or n (%). NSIP: nonspecific interstitial pneumonia; COP: crytogenic organising pneumonia; IPF: idiopathic pulmonary fibrosis; UCTD: undifferentiated connective tissue disease; ILD: interstitial lung disease.