TABLE 1

Reported median survival and numbers of children and adults with cystic fibrosis from selected registries

CountryYear of annual reportMedian age at death yearsMedian predicted age of survival yearsPercentage of adult patients (≥18 years)Total number of patients
Belgium2011#33NA54.71171
Denmark2010 (ECFSPR)#33NA56.8450
France201228NA47.26196
Germany201232NA52.45242
UK20122843.557.6+10 078§
Australia201229NA49.33156
Canada20123249.758.83975
USA2012NA41.149.127 804
  • #: age computed from the 2010 European Cystic Fibrosis Society patient registry (ECFSPR) data; : patients whose vital status is known, whether they visited the cystic fibrosis centre or not; +: ≥16 years; §: all patients. NA: not available.