Patient characteristics at baseline and change at 1 and 6 months follow-up

BaselinePer cent predicted at baselineΔ1 month from baselineΔ6 months from baseline
Subjects n11511511086
Age years60±8.8NANANA
BMI kg·m−224±3.6NA0.3±0.80.5±1.1
6MWD m311±95NA38.5±60.738.2±68.5
SGRQ total score units62±10.9NA−9.8±13.8−7.5±15.8
RV L4.9±1.1241±46.7−0.5±0.6−0.5±0.6
FEV1 L0.7±0.325.9±9.00.1±0.20.1±0.2
TLC L7.7±1.4136±14.6−0.2±0.4−0.25±0.4
RV/TLC %64.6±7.7168±22.2−4.0±5.7−4.1±6.3
  • Data are presented as n or mean±sd. Δ: change between baseline and follow-up; BMI: body mass index; FEV1: forced expiratory volume in 1 s; 6MWD: 6-min walk distance; SGRQ: St George's Respiratory Questionnaire; RV: residual volume; TLC: total lung capacity; NA: not applicable.