Table 25

Recommendations for pulmonary arterial hypertension associated with congenital heart disease

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  • CCBs: calcium channel blockers; ERAs: endothelin receptor antagonists; O2: oxygen; PA: pulmonary artery; PDE-5is: phosphodiesterase type 5 inhibitors; WHO-FC: World Health Organization functional class.

  • aClass of recommendation.

  • bLevel of evidence.

  • cReference(s) supporting recommendations.