CTEPH: chronic thromboembolic pulmonary hypertension; Echo: echocardiographic; PAH: pulmonary arterial hypertension; PH: pulmonary hypertension; RHC: right heart catheterization.
aClass of recommendation.
bLevel of evidence.
cReference(s) supporting recommendations.
dThese recommendations do not apply to patients with diffuse parenchymal lung disease or left heart disease.
eDepending on the presence of risk factors for PH group 2, 3 or 5.
Further investigation strategy may differ depending on whether risk factors/associated conditions suggest higher probability of PAH or CTEPH – see diagnostic algorithm.