Cause of death
| All patients | IPAH/HPAH | PAH-CHD | PAH-CTD | |
| Patients | 192 | 102 | 61 | 29 |
| Death | 66 | 34 | 17 | 15 |
| Heart failure | 40 | 17 | 11 | 12 |
| Sudden death | 9 | 4 | 4 | 1 |
| Haemoptysis | 4 | 3 | 1 | 0 |
| Respiratory failure | 3 | 3 | 0 | 0 |
| Infection | 3 | 1 | 1 | 1 |
| Other | 3 | 0 | ||
| Neoplasia | 1 | |||
| Myocardial infarction | 1 | |||
| Renal failure | 1 | |||
| Unknown | 4 | 4 | 0 | 0 |
Data are presented as n. PAH: pulmonary arterial hypertension; IPAH: idiopathic PAH; HPAH: heritable PAH; CHD: congenital heart disease; CTD: connective tissue disease.