Parameters of the REVEAL registry PAH risk score calculator
| Parameter | Value |
| WHO group 1 subgroup | |
| APAH-CTD | +1 |
| APAH-PoPH | +2 |
| FPAH | +2 |
| Demographics and comorbidities | |
| Renal insufficiency | +1 |
| Males aged >60 years | +2 |
| NYHA/WHO functional class | |
| I | −2 |
| III | +1 |
| IV | +2 |
| Vital signs | |
| Systolic blood pressure <110 mmHg | +1 |
| Heart rate >92 beats·min−1 | +1 |
| 6-min walking distance | |
| ≥440 m | −1 |
| <165 m | +1 |
| BNP# | |
| <50 pg·mL−1 | −2 |
| >180 pg·mL−1 | +1 |
| Echocardiogram | |
| Pericardial effusion | +1 |
| Pulmonary function test | |
| DLCO ≥80% predicted | −1 |
| DLCO ≤32% predicted | +1 |
| Right heart catheterisation | |
| Mean RAP >20 mmHg within 1 year | +1 |
| PVR >32 Wood units | +2 |
REVEAL: Registry to Evaluate Early and Long-term PAH Disease Management; PAH: pulmonary arterial hypertension; WHO: World Health Organization; APAH: associated with PAH; CTD: connective tissue disease; PoPH: portopulmonary hypertension; FPAH: familial PAH; NYHA: New York Heart Association; BNP: brain natriuretic peptide; DLCO: diffusing capacity of the lung for carbon monoxide; RAP: right atrial pressure; PVR: pulmonary vascular resistance. #: if N-terminal proBNP is available and BNP is not, listed cut-points are replaced with <300 pg·mL−1 and >1500 pg·mL−1.