| Subjects n | 4886 |
| Newly diagnosed cases n | 1498 |
| Females | 46.9 |
| Caucasians | 92.8 |
| Age at last visit years | 22.0 (0–79.3) |
| Age at diagnosis years median | 0.5 |
| Age at diagnosis | |
| 0–2 years | 66.8 |
| 2–18 years | 26.2 |
| >18 years | 6.9 |
| Genotype | |
| Homozygous ΔF508 | 48.1 |
| Heterozygous ΔF508 | 38.1 |
| Other | 9.9 |
| Missing | 4.0 |
| FEV1% predicted | 67.7 (9.5–145.1) |
| BMI category | |
| Normal weight | 59.0 |
| Overweight | 13.4 |
| Underweight | 17.9 |
| Missing | 9.8 |
| Microbiology¶ | |
| Pseudomonas aeruginosa | 79.3 |
| Staphylococcus aureus | 87.8 |
| Stenotrophomonas maltophilia | 37.8 |
| Burkholderia cepacia complex | 11.6 |
| MRSA | 9.0 |
| Pancreatic insufficiency | 85.9 |
| CF-related diabetes | 24.1 |
| Region+ | |
| Quebec | 29.1 |
| East | 9.1 |
| Ontario | 34.5 |
| West | 27.3 |
| Exacerbations per year | |
| 0 | 68.6 |
| 1–2 | 21.2 |
| ≥3 | 10.2 |
| Transplants | 472 (9.7) |
| Males | 255 |
| Females | 217 |
| Total deaths n | 485 |
| Males | 227 (46.6) |
| Females | 260 (53.4) |
Data are presented as %, median (range) or n (%), unless otherwise stated. FEV1: forced expiratory volume in 1 s; BMI: body mass index; MRSA: methicillin-resistant S. aureus; CF: cystic fibrosis. #: last recorded measurement used to summarise the data; ¶: reflects the proportion of individuals who ever had a positive sputum culture in the study period; +: based on the region in which the subject spent the longest time.