TABLE 2

Proportions of tuberous sclerosis complex (TSC) and sporadic lymphangioleiomyomatosis (LAM) patients with functional abnormalities

TSC–LAMSporadic LAMp-value#
Patients n94460
Airflow obstruction31 (32.9)234 (50.8)0.002
Diffusion abnormality38 (40.4)282 (61.3)<0.001
Airflow obstruction and diffusion abnormality25 (26.5)194 (42.1)0.005
Normal pulmonary function40 (42.5)122 (26.5)0.002