Study | PCD | Healthy controls | Cystic fibrosis | |||
Subjects n | Outcome nL·min−1 | Subjects n | Outcome nL·min−1 | Subjects n | Outcome nL·min−1 | |
Karadag et al. [6], 1999 | 21 | Median 13.75 (range 0.83–239.8) | 60 | Median 138.3 (range 29–359.3) | ||
Narang et al. [7], 2002 | 31 | Median 15.1 (range 0.8–230) | 53 | Median 179 (range 99.5–359.3) | 17 | Median 122.8 (range 7.8–285) |
Horvath et al. [8], 2003 | 14 | Median 13.6 (range 1.3–67.3) | 37 | Median 165.8 (range 80.5–335.8) | 20 | Median 85.8 (range 7.5–249.3) |
Santamaria et al. [29], 2008 | 14 | Median 3.3 (IQR 3.3) | 14 | Median 90.1 (IQR 67.2) | ||
Marthin and Nielsen [25], 2011# | 12 | Median 15.9 (95% CI 3–162) | ||||
Walker et al. [30], 2013 | 14 | Median 8.1 (IQR 4.8–22.8) | 18 | Median 231.6 (IQR 207–265.8) | 12 | Median 150.3 (IQR 135–182.4) |
Boon et al. [31], 2014 | 38 | Median 16.8 (IQR 8.1–35.7) | 49 | Median 236.4 (IQR 198.3–295.8) | 46 | Median 109.5 (IQR 75.6–169.5) |
Harris et al. [32], 2014 | 11 | Median 12.3 (IQR 7.5–15.9) | 15 | 208.2 (IQR 181.2–240) | 6 | Median 139.5 (IQR 99–227.7) |
PCD: primary ciliary dyskinesia; IQR: interquartile range. #: consecutive referrals.