Subjects | 30 |
Females/males | 18/12 |
Age years | 56.3±38 (26–80) |
Aetiology of PH | |
Group 1: PAH | |
Idiopathic | 12 |
Connective tissue disease | 7 |
Congenital heart disease | 5 |
Heritable | 1 |
Portal hypertension | 1 |
Drugs/toxins | 1 |
Group 3: owing to respiratory disease in PH lung | 1 |
Group 4: CTEPH | 2 |
Time since PAH diagnosis years | |
<1 | 2 |
1 to <3 | 2 |
3 to <5 | 7 |
5 to <10 | 12 |
>10 | 7 |
WHO functional class | |
I | 0 |
II | 9 |
III | 19 |
IV | 2 |
Data are presented as n or mean±sd (range). PH: pulmonary hypertension; PAH: pulmonary arterial hypertension; CTEPH: chronic thromboembolic PH; WHO: World Health Organization.