BMD# | DMD¶ | Wilcoxon p-value | |
Age years | 12.5 (5.4–16.4) | 11.0 (5.0–16.7) | 0.1500 |
Height cm | 149 (116–181) | 136 (103–170) | 0.0430 |
Weight kg | 43.8 (22.0–93.0) | 29.5 (17.0–80) | 0.0540 |
BMI kg·m−2 | 20.1 (15.2–33.7) | 16.5 (12.5–33.8) | 0.0540 |
BMI z-score+ | 0.2 (−0.7–4.8) | −0.1 (−4.8–6.3) | 0.2200 |
Raw data | |||
SNIP cmH2O | 72 (45–148) | 48 (22–80) | 0.0003 |
PImax cmH2O | 76 (44–146) | 38 (17–75) | 0.0008 |
Slow VC L | 2.62 (1.45–5.36) | 1.70 (0.77–2.11) | <0.0001 |
SNIP/PImax | 1.08 (0.59–1.71) | 1.17 (0.65–2.35) | 0.2440 |
Z-scores | |||
SNIP | −1.40 (−3.26–1.05) | −2.20 (−4.24– −0.91) | 0.0055 |
PImax | −0.91 (−3.91–1.57) | −2.63 (−5.27– −0.28) | 0.0178 |
VC | −1.19 (−1.81–0.00) | −2.20 (−6.25–1.23) | 0.0259 |
Data are presented as median (range), unless otherwise stated. Values are expressed as raw values, or as z-scores i.e. ((recorded−predicted)/residual standard deviation from regression line of reference values). BMD: Becker muscular dystrophy; DMD: Duchenne muscular dystrophy; BMI: body mass index; SNIP: sniff nasal inspiratory pressure; PImax: maximal inspiratory pressure; VC: vital capacity. #: n = 10; ¶: n = 33; +: calculated according to [15].