Table 1– Baseline data of the 43 children included in the study
BMD#DMDWilcoxon p-value
Age years12.5 (5.4–16.4)11.0 (5.0–16.7)0.1500
Height cm149 (116–181)136 (103–170)0.0430
Weight kg43.8 (22.0–93.0)29.5 (17.0–80)0.0540
BMI kg·m−220.1 (15.2–33.7)16.5 (12.5–33.8)0.0540
BMI z-score+0.2 (−0.7–4.8)−0.1 (−4.8–6.3)0.2200
Raw data
 SNIP cmH2O72 (45–148)48 (22–80)0.0003
PImax cmH2O76 (44–146)38 (17–75)0.0008
 Slow VC L2.62 (1.45–5.36)1.70 (0.77–2.11)<0.0001
 SNIP/PImax1.08 (0.59–1.71)1.17 (0.65–2.35)0.2440
Z-scores
 SNIP−1.40 (−3.26–1.05)−2.20 (−4.24– −0.91)0.0055
PImax−0.91 (−3.91–1.57)−2.63 (−5.27– −0.28)0.0178
 VC−1.19 (−1.81–0.00)−2.20 (−6.25–1.23)0.0259
  • Data are presented as median (range), unless otherwise stated. Values are expressed as raw values, or as z-scores i.e. ((recorded−predicted)/residual standard deviation from regression line of reference values). BMD: Becker muscular dystrophy; DMD: Duchenne muscular dystrophy; BMI: body mass index; SNIP: sniff nasal inspiratory pressure; PImax: maximal inspiratory pressure; VC: vital capacity. #: n = 10; : n = 33; +: calculated according to [15].