Table 1– Selected Cystic Fibrosis Questionnaire-revised (CFQ-R) scores for children, their parents and adolescents
Children (6–13 years)Adolescents (≥14 years)
CFQ-R Child versionCFQ-R Parent versionCFQ-R Teen/Adult version
Subjects403732
Respiratory symptoms83 (50–100)89 (50–100)77 (11–100)
Physical functioning83 (39–100)93 (52–100)90 (38–100)
Vitality73 (47–93)67 (25–100)
Health perceptions78 (22–100)67 (22–100)
  • Data are presented as n or median (range). CFQ-R scale scores are shown for the different versions of the CFQ-R. The CFQ-R respiratory symptoms scale was the primary target. Physical functioning, vitality and health perceptions were secondary domains correlating with forced expiratory volume in 1 s. For each domain, a score of 0–100 is calculated. Higher scores indicate better health-related quality of life.