| Variable | Baseline | 6-month follow up | p-value |
| RV % pred | 223 (184–267) | 205 (134–223) | 0.001 |
| RV/TLC % | 61.4 (55.4–67.4) | 56.7 (48.3–65.3) | 0.008 |
| FEV1 % pred | 28 (22–42) | 32 (15–58) | 0.35 |
| mMRC score | 3 (2–4) | 2 (2–4) | 0.06 |
| 6MWD m | 336 (200–451) | 348 (140–477) | 0.22 |
| Activity % | 17.6 (8.1–27.9) | 15.0 (7.7–26.4) | 0.29 |
| Steps per day | 2084 (374–5800) | 2426 (321–5721) | 0.68 |
| Physical activity level | 1.51 (1.33–1.61) | 1.50 (1.37–1.66) | 0.55 |
| Self-efficacy, LIVAS total score | 29 (13–39) | 30 (20–42) | 0.28 |
Data are presented as median (range), unless otherwise stated. RV: residual volume; % pred: % predicted; TLC: total lung capacity; FEV1: forced expiratory volume in 1 s; mMRC: modified Medical Research Council dyspnoea index; 6MWD: 6-min walk distance. Baseline and follow-up measurements were compared with Wilcoxon signed-rank test (significant p-values are shown in bold).